Cystic Fibrosis (CF)

CF is a genetic disorder of the exocrine glands causing the abnormal production of thick mucus. The thick mucus leads to blockages within the pancreatic ducts, intestines, and bronchi. 

There is a lack of high quality evidence to support nutritional recommendations for infants newly diagnosed with CF. It is appropriate that infants identified with CF be given the opportunity to participate in randomized controlled trials where available to increase evidence-based research.

Exclusive breastfeeding is recommended for infants with CF but infants may need to be supplemented with pancreatic enzymes. Enzyme therapy can be delivered via supplemental nursing system. Research shows that exclusively breastfed infants with CF had better weight gain and growth outcomes than other feeding choices (Holliday et al., 1991). Studies have also found that human milk feedings help to protect the baby with CF from infections.

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